Show obsolete/secondary identifiers |
Mutation Data |
LS-SNP | | SNP Information available through LS-SNP |
Template Structure |
---|
PDB | 2bff | reactivity modulation of human branched-chain alpha-ketoacid dehydrogenase by an internal molecular switch |
DBALI | 2bffA | |
CATH | 3.40.50.970 | Domain: 2bffA00 Rossmann fold (83%) |
JenaImageLibrary | 2bff | |
Target Sequence |
---|
UniProtKB | G3RCK8 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | G3RCK8 | |
PFAM | G3RCK8 | |
Prodom | G3RCK8 | |
UniProtKB | F7HBM4 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | F7HBM4 | |
PFAM | F7HBM4 | |
Prodom | F7HBM4 | |
UniProtKB | Q9UBU0 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UBU0 | |
PFAM | Q9UBU0 | |
Prodom | Q9UBU0 | |
UniProtKB | G1RFJ2 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | G1RFJ2 | |
PFAM | G1RFJ2 | |
Prodom | G1RFJ2 | |
UniProtKB | Q9UNG4 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UNG4 | |
PFAM | Q9UNG4 | |
Prodom | Q9UNG4 | |
UniProtKB | Q9UNG5 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UNG5 | |
PFAM | Q9UNG5 | |
Prodom | Q9UNG5 | |
UniProtKB | A0A024RBX9 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | A0A024RBX9 | |
PFAM | A0A024RBX9 | |
Prodom | A0A024RBX9 | |
UniProtKB | H2QYD5 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | H2QYD5 | |
PFAM | H2QYD5 | |
Prodom | H2QYD5 | |
UniProtKB | F7H490 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139};EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139}; |
InterPro | F7H490 | |
PFAM | F7H490 | |
Prodom | F7H490 | |
UniProtKB | G3RCK8 | SubName: Full=Uncharacterized protein; |
InterPro | G3RCK8 | |
PFAM | G3RCK8 | |
Prodom | G3RCK8 | |
UniProtKB | F7HBM4 | SubName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1;SubName: Full=Uncharacterized protein; |
InterPro | F7HBM4 | |
PFAM | F7HBM4 | |
Prodom | F7HBM4 | |
UniProtKB | F7H490 | SubName: Full=Uncharacterized protein; |
InterPro | F7H490 | |
PFAM | F7H490 | |
Prodom | F7H490 | |
UniProtKB | A0A6J3III1 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A6J3III1 | |
PFAM | A0A6J3III1 | |
Prodom | A0A6J3III1 | |
UniProtKB | A0A6D2WWB4 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A6D2WWB4 | |
PFAM | A0A6D2WWB4 | |
Prodom | A0A6D2WWB4 | |
UniProtKB | A0A2K5PQV9 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A2K5PQV9 | |
PFAM | A0A2K5PQV9 | |
Prodom | A0A2K5PQV9 | |
UniProtKB | A0A2K5P3B4 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A2K5P3B4 | |
PFAM | A0A2K5P3B4 | |
Prodom | A0A2K5P3B4 | |
UniProtKB | A0A2J8W447 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A2J8W447 | |
PFAM | A0A2J8W447 | |
Prodom | A0A2J8W447 | |
UniProtKB | A0A2I2Y5G2 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A2I2Y5G2 | |
PFAM | A0A2I2Y5G2 | |
Prodom | A0A2I2Y5G2 | |
UniProtKB | A0A2J8IZ93 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | A0A2J8IZ93 | |
PFAM | A0A2J8IZ93 | |
Prodom | A0A2J8IZ93 | |
UniProtKB | H2PV27 | SubName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial; |
InterPro | H2PV27 | |
PFAM | H2PV27 | |
Prodom | H2PV27 | |
UniProtKB | H2QYD5 | SubName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial; |
InterPro | H2QYD5 | |
PFAM | H2QYD5 | |
Prodom | H2QYD5 | |
UniProtKB | U3FGT0 | Pyruvate dehydrogenase E1 component subunit alpha {ECO:0000256|RuleBase:RU361139}EC=1.2.4.1 {ECO:0000256|RuleBase:RU361139} |
InterPro | U3FGT0 | |
PFAM | U3FGT0 | |
Prodom | U3FGT0 | |
UniProtKB | Q5JPT8 | SubName: Full=Pyruvate dehydrogenase (Lipoamide) alpha 1;SubName: Full=Pyruvate dehydrogenase (Lipoamide) alpha 1, isoform CRA_a; |
InterPro | Q5JPT8 | |
PFAM | Q5JPT8 | |
Prodom | Q5JPT8 | |
UniProtKB | Q9UNG5 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UNG5 | |
PFAM | Q9UNG5 | |
Prodom | Q9UNG5 | |
UniProtKB | Q9UNG4 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UNG4 | |
PFAM | Q9UNG4 | |
Prodom | Q9UNG4 | |
UniProtKB | Q9UBU0 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UBU0 | |
PFAM | Q9UBU0 | |
Prodom | Q9UBU0 | |
UniProtKB | Q9UBJ8 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9UBJ8 | |
PFAM | Q9UBJ8 | |
Prodom | Q9UBJ8 | |
UniProtKB | Q9NP12 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q9NP12 | |
PFAM | Q9NP12 | |
Prodom | Q9NP12 | |
UniProtKB | Q5JPT8 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q5JPT8 | |
PFAM | Q5JPT8 | |
Prodom | Q5JPT8 | |
UniProtKB | Q53H41 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | Q53H41 | |
PFAM | Q53H41 | |
Prodom | Q53H41 | |
UniProtKB | P08559.3 | ODPA_HUMAN RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial; AltName: Full=PDHE1-A type I; Flags: Precursor |
InterPro | P08559.3 | |
PFAM | P08559.3 | |
Prodom | P08559.3 | |
UniProtKB | P08559 | RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;EC=1.2.4.1;AltName: Full=PDHE1-A type I;Flags: Precursor; |
InterPro | P08559 | |
PFAM | P08559 | |
Prodom | P08559 | |
RefSeq | NP_000275.1 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1 precursor [Homo sapiens] |
RefSeq | XP_003819601.1 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial |
RefSeq | XP_011781591.1 | PREDICTED: pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform X1 |
GenPept | 14762225 | pyruvate dehydrogenase (lipoamide) alpha 1 [Homo sapiens] |
GenPept | 119619367 | pyruvate dehydrogenase (lipoamide) alpha 1, isoform CRA_a |
GenPept | 219982 | pyruvate dehydrogenase alpha subunit |
GenPept | 292413 | pyruvate dehydrogenase E1-alpha subunit |
GenPept | 353306103 | Sequence 68 from patent US 8039587 |
GenPept | 35379 | unnamed protein product |
GenPept | 358782496 | Sequence 68 from patent US 8062891 |
GenPept | 380813630 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1 precursor |
GenPept | 383419059 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1 precursor |
GenPept | 384947596 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1 precursor |
GenPept | 387009 | pyruvate dehydrogenase E1-alpha subunit |
GenPept | 190762 | pyruvate dehydrogenase alpha subunit precursor (EC 1.2.4.1) |
GenPept | 189738 | pyruvate dehydrogenase alpha subunit |
GenPept | 123981924 | pyruvate dehydrogenase (lipoamide) alpha 1 |
GenPept | 123996757 | pyruvate dehydrogenase (lipoamide) alpha 1, partial |
GenPept | 123996763 | pyruvate dehydrogenase (lipoamide) alpha 1, partial |
GenPept | 12803199 | Pyruvate dehydrogenase (lipoamide) alpha 1 |
GenPept | 129063 | ODPA_HUMAN RecName: Full=Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial; AltName: Full=PDHE1-A type I; Flags: Precursor |
GenPept | 14762191 | pyruvate dehydrogenase (lipoamide) alpha 1 [Homo sapiens] |
GenPept | 14762207 | pyruvate dehydrogenase (lipoamide) alpha 1 [Homo sapiens] |
GenPept | 14762211 | pyruvate dehydrogenase (lipoamide) alpha 1 [Homo sapiens] |
GenPept | 119619366 | pyruvate dehydrogenase (lipoamide) alpha 1, isoform CRA_a |
GenPept | 42683589 | Sequence 5 from patent US 6677144 |
GenPept | 4505685 | pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial isoform 1 precursor [Homo sapiens] |
GenPept | 549828337 | Sequence 68 from patent US 8541550 |
GenPept | 56577252 | Sequence 36 from patent US 6773917 |
GenPept | 568533841 | Sequence 19606 from patent US 8586006 |
GenPept | 57209621 | pyruvate dehydrogenase (lipoamide) alpha 1 |
GenPept | 649102011 | PDHA1, partial |
GenPept | 66034 | DEHUPA pyruvate dehydrogenase (lipoamide) (EC 1.2.4.1) alpha chain precursor - human |
GenPept | 35381 | unnamed protein product |
GenPept | 534490753 | Sequence 68 from patent US 8507277 |
GenPept | 516171713 | Sequence 68 from patent US 8470972 |
GenBank | AAA60050.1 | pyruvate dehydrogenase alpha subunit [Homo sapiens] |
GenBank | AAA60051.1 | pyruvate dehydrogenase E1-alpha subunit [Homo sapiens] |
GenBank | AAA60227.1 | pyruvate dehydrogenase E1-alpha subunit [Homo sapiens] |
GenBank | AAH02406.1 | Pyruvate dehydrogenase (lipoamide) alpha 1 [Homo sapiens] |
GenBank | ABM82791.1 | pyruvate dehydrogenase (lipoamide) alpha 1 [synthetic construct] |
GenBank | EAW98961.1 | pyruvate dehydrogenase (lipoamide) alpha 1, isoform CRA_a [Homo sapiens] |
GenBank | EAW98960.1 | pyruvate dehydrogenase (lipoamide) alpha 1, isoform CRA_a [Homo sapiens] |
GenBank | AAA36533.1 | pyruvate dehydrogenase alpha subunit precursor (EC 1.2.4.1) [Homo sapiens] |
GenBank | ABM85983.1 | pyruvate dehydrogenase (lipoamide) alpha 1 [synthetic construct] |
GenBank | ABM85980.1 | pyruvate dehydrogenase (lipoamide) alpha 1 [synthetic construct] |
ENSEMBL | ENSP00000254142 | Pyruvate dehydrogenase E1 component alpha subunit, somatic form, mitochondrial precursor (EC 1.2.4.1) (PDHE1-A type I). [Homo sapiens] |
EMBL | CAA36934.1 | |
EMBL | CAA36933.1 | |
EMBL | CAI41291.1 | |
UCSCGenomeBrowser | P08559 | |
UCSCGenomeBrowser | ENSPTRT00000040292.1 | |
ENSEMBL | ENSP00000254142 | |
ENSEMBL | ENSPTRP00000037227 | |
ENSEMBL | ENSP00000254142 | TDI sequence |
ENSEMBL | ENSP00000394382 | |
|